Search on: FAMILIAL IDIOPATHIC CARDIOMYOPATHY 
Descriptors Found: 1
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 1 / 1 DeCS     
Descriptor English:   Cardiomyopathy, Dilated 
Descriptor Spanish:   Cardiomiopatía Dilatada 
Descriptor Portuguese:   Cardiomiopatia Dilatada 
Synonyms English:   1As, Dilated cardiomyopathy
Cardiomyopathies, Congestive
Cardiomyopathies, Dilated
Cardiomyopathies, Familial Idiopathic
Cardiomyopathies, Idiopathic Dilated
Cardiomyopathy, Congestive
Cardiomyopathy, Dilated, 1a
Cardiomyopathy, Dilated, Autosomal Recessive
Cardiomyopathy, Dilated, CMD1A
Cardiomyopathy, Dilated, LMNA
Cardiomyopathy, Dilated, With Conduction Defect 1
Cardiomyopathy, Dilated, with Conduction Deffect1
Cardiomyopathy, Familial Idiopathic
Cardiomyopathy, Idiopathic Dilated
Congestive Cardiomyopathies
Congestive Cardiomyopathy
Dilated Cardiomyopathies
Dilated Cardiomyopathies, Idiopathic
Dilated Cardiomyopathy
Dilated Cardiomyopathy, Idiopathic
Dilated cardiomyopathy 1A
Dilated cardiomyopathy 1As
Familial Idiopathic Cardiomyopathies
Familial Idiopathic Cardiomyopathy
Idiopathic Cardiomyopathies, Familial
Idiopathic Cardiomyopathy, Familial
Idiopathic Dilated Cardiomyopathies
Idiopathic Dilated Cardiomyopathy
cardiomyopathy 1A, Dilated
cardiomyopathy 1As, Dilated  
Tree Number:   C14.280.195.160
C14.280.238.070
Definition English:   A form of CARDIAC MUSCLE disease that is characterized by ventricular dilation, VENTRICULAR DYSFUNCTION, and HEART FAILURE. Risk factors include SMOKING; ALCOHOL DRINKING; HYPERTENSION; INFECTION; PREGNANCY; and mutations in the LMNA gene encoding LAMIN TYPE A, a NUCLEAR LAMINA protein. 
Indexing Annotation English:   note entry term CARDIOMYOPATHY, CONGESTIVE: do not confuse with HEART FAILURE
History Note English:   2005 (1984) 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   2355 
Unique Identifier:   D002311 

Occurrence in VHL:
 

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